Pediatric Neurology
Volume 25, Issue 1 , Pages 75-77 , July 2001

Moyamoya syndrome with spherocytosis: effect of splenectomy on strokes

  • Yoichi Tokunaga, MD

      Affiliations

    • Department of Pediatrics; Graduate School of Medical Sciences; Kyushu University; Fukuoka, Japan
    • ,
  • Shouichi Ohga, MD

      Affiliations

    • Department of Pediatrics; Graduate School of Medical Sciences; Kyushu University; Fukuoka, Japan
    • Corresponding Author InformationCommunications should be addressed to: Dr. Ohga; Department of Pediatrics; Faculty of Medicine; Kyushu University; 3-1-1 Maidashi; Higashi-ku; Fukuoka 812-8582; Japan
    • ,
  • Sachiyo Suita, MD

      Affiliations

    • Department of Pediatric Surgery; Graduate School of Medical Sciences; Kyushu University; Fukuoka, Japan
    • ,
  • Toshio Matsushima, MD

      Affiliations

    • Department of Neurosurgery; Graduate School of Medical Sciences; Kyushu University; Fukuoka, Japan
    • ,
  • Toshiro Hara, MD

      Affiliations

    • Department of Pediatrics; Graduate School of Medical Sciences; Kyushu University; Fukuoka, Japan

Received 14 December 2000 ,Accepted 19 March 2001.

References 

  1. Suzuki J, Takaku A. Cerebrovascular. “moyamoya” disease. Disease showing abnormal net-like vessels in base of brain. Arch Neurol. 1969;20:288–299
  2. Kurokawa T, Tomita S, Ueda K, et al.  Prognosis of occlusive disease of the circle of Willis (Moyamoya disease) in children. Pediatr Neurol. 1985;1:274–277
  3. Matsushima Y, Aoyagi M, Nariai T, Takada Y, Hirokawa K. Long-term intelligence outcome of post-encephalo-duro-arteri-synangiosis in childhood Moyamoya patients. Clin Neurol Neurosurgery. 1997;99(Suppl 2):S147–S150
  4. Gallagher PG, Forget BG. Hematologically important mutations (Spectrin and ankyrin variants in hereditary spherocytoisis). Blood Cells Mol Dis. 1998;24:539–543
  5. Ohene-Frempong K, Weiner SJ, Sleeper LA, et al.  Cerebrovascular accidents in sickle cell disease (Rates and risk factors). Blood. 1998;91:288–294
  6. Holz A, Woldenberg R, Miller D, Kalina P, Black K, Lane E. Moyamoya disease in a patient with hereditary spherocytosis. Pediatr Radiol. 1998;28:95–97
  7. Grotta JC, Manner C, Pettigrew LC, Yatsu FM. Red blood cell disorders and stroke. Stroke. 1986;17:811–817
  8. Stockman JA, Nigro MA, Mishkin MM, Oski FA. Occlusion of large cerebral vessels in sickle-cell anemia. N Engl J Med. 1972;287:846–849
  9. van Hilten JJ, Haan J, Wintzen AR, et al.  Cerebral infarction in hereditary spherocytosis. [letter] Stroke. 1989;20:1755–1756
  10. Peerless SJ. Risk factors of moyamoya disease in Canada and the USA. Clin Neuro Neurosurg. 1997;99(Suppl 2):S45–S48
  11. Mukherjee A. Moyamoya disease and β-thalassemia. J Assoc Physician India. 1995;43:710–711
  12. Cohen N, Berant M, Simon J. Moyamoya and Fanconi’s anemia. Pediatrics. 1980;65:804–805
  13. Schilling RF. Spherocytosis, splenectomy, strokes, and heart attacks. Lancet. 1997;350:1677–1678
  14. Hayag-Barin JE, Smith RE, Tucker FC. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli (A case report and review of the literature). Am J Hematol. 1998;57:82–84
  15. Bruguier A, Clement MC, Texier P, Ponsot G. Cerebral ischemic accident and hereditary spherocytosis. Arch Franc Pediatr. 1983;40:653–654
  16. Hartfield DS, Lowry NJ, Keene DL, Tager JY. Iron deficiency (A cause of stroke in infants and children). Pediatr Neurol. 1997;16:50–53
  17. Adams RJ, McKie VC, Hsu L, et al.  Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography. N Engl J Med. 1998;339:5–11

PII: S0887-8994(01)00283-1

Pediatric Neurology
Volume 25, Issue 1 , Pages 75-77 , July 2001

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