Medulloblastoma or cerebellar dysplastic gangliocytoma (Lhermitte-Duclos disease)?

Chen, Kuo-Shin; Hung, Po-Cheng; Wang, Huei-Shyong; Jung, Shih-Ming; Ng, Shu-Hang

« Previous Next »Pediatric Neurology
Volume 27, Issue 5 , Pages 404-406, November 2002

Medulloblastoma or cerebellar dysplastic gangliocytoma (Lhermitte-Duclos disease)?

Kuo-Shin Chen, MD
- Division of Pediatric Neurology; Chang Gung Children’s Hospital; Medical College of Chang Gung University; Taoyuan, Taiwan
Po-Cheng Hung, MD
- Division of Pediatric Neurology; Chang Gung Children’s Hospital; Medical College of Chang Gung University; Taoyuan, Taiwan
Huei-Shyong Wang, MD
- Division of Pediatric Neurology; Chang Gung Children’s Hospital; Medical College of Chang Gung University; Taoyuan, Taiwan
- Communications should be addressed to: Dr. Wang; Division of Pediatric Neurology; Chang Gung Children’s Hospital; 5-7, Fu-Hsin Street; Kueishan; Taoyuan, 333 Taiwan.
Shih-Ming Jung, MD
- Departments of Pathology, Chang Gung Memorial Hospital; Medical College of Chang Gung University, Taoyuan, Taiwan
Shu-Hang Ng, MD
- Diagnostic Radiology, Chang Gung Memorial Hospital; Medical College of Chang Gung University, Taoyuan, Taiwan

Received 26 February 2002; accepted 22 May 2002.

Abstract

Dysplastic cerebellar gangliocytoma is a rare benign tumor associated with specific neuroimaging findings of abnormal laminated or folial pattern in the posterior fossa. Some authors thus proposed that it could be diagnosed by neuroimaging studies alone. We encountered a patient with medulloblastoma in which the neuroimaging findings mimicked those of dysplastic gangliocytoma. In patients with a posterior fossa tumor suggestive of a dysplastic gangliocytoma on neuroimaging studies, a pathologic confirmation is necessary.