Pediatric Neurology
Volume 43, Issue 1 , Pages 46-48, July 2010

Bilateral Striopallidodentate Calcinosis With Paroxysmal Kinesigenic Dyskinesia

  • Gloria E. Diaz, MD

      Affiliations

    • Division of Child and Adolescent Neurology, Mayo Clinic, Rochester, Minnesota
    • Corresponding Author InformationCommunications should be addressed to: Dr. Diaz; Division of Child and Adolescent Neurology, Department of Neurology; Mayo Clinic; 200 First Street Southwest; Rochester, MN 55905.
    • ,
  • Elaine C. Wirrell, MD

      Affiliations

    • Division of Child and Adolescent Neurology, Mayo Clinic, Rochester, Minnesota
    • ,
  • Joseph Y. Matsumoto, MD

      Affiliations

    • Division of Movement Disorders, Department of Neurology, Mayo Clinic, Rochester, Minnesota
    • ,
  • Karl N. Krecke, MD

      Affiliations

    • Department of Radiology, Mayo Clinic, Rochester, Minnesota

Received 14 November 2009; accepted 15 March 2010.

Bilateral striopallidodentate calcinosis is characterized by calcification of the basal ganglia and other gray matter structures. We describe a 16-year-old boy with paroxysmal kinesigenic dyskinesia. He exhibited mineralization in the basal ganglia, posterior thalami, and dentate nuclei bilaterally, and was diagnosed with sporadic bilateral striopallidodentate calcinosis. The paroxysmal kinesigenic dyskinesia responded to low-dose treatment with carbamazepine (200 mg/day).

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PII: S0887-8994(10)00145-1

doi:10.1016/j.pediatrneurol.2010.03.013

Pediatric Neurology
Volume 43, Issue 1 , Pages 46-48, July 2010

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